Volume 32 Number 2 (2023)

A Case of Congenital Coronary Ostial Stenosis with Systemic Lupus Erythematosus

Habib SA1 , Fatema N2 , Alam MM3 , Ahasan SA4 , Rahman MF5 , Ear-E-Mahabub SM6 , Akand AI7 , Singha CK8 , Anwar AA9 , Khondoker MN10 , Islam MA11

Mymensingh Med J 2023 Apr; 32 (2): 590-592

PMID: 37002776

Abstract

Congenital coronary ostial stenosis or atresia (COSA) is a spectrum of rare developmental conditions with different pathophysiologic mechanisms and clinical implications. Although COSA includes various entities, these entities have two features in common. First the defect is congenital, although it may progress during pre-natal and post natal life. Second the developmental defect may cause ostial or proximal coronary obstruction (that is stenosis or atresia). Coronary ostial stenosis or atresia affects the left coronary (L-COSA) more frequently than it does the right coronary artery. Systemic Lupus Erythematosus (SLE) is not an uncommon disease in young female, but combination of congenital coronary ostial stenosis with systemic lupus erythematosus make the case very rarer. Here we presented A 17 years old girl got admitted to Bangabandhu Sheikh Mujib Medical University, Bangladesh for evaluation of on and off chest pain of CCS-III to CCS-IV for 1 day on 17 September 2019.

Keywords: Congenital ostial stenosis (COSA), Systemic lupus erythematosus (SLE)


  1. Associate Professor

    Department of Cardiology, University Cardiac Centre, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh

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Volume 32, Number 2 (2023)
Page: 590-592